Lipoid proteninosis:case report
نویسندگان
چکیده مقاله:
URBACH-WIETHE is a very rare autosomally recessive disorder characterized by infiltration of hyaline material into skin,oral cavity,larynx,and internal organs.in this report we persent a case of a 22 year old woman with small scars on her face,hoarseness,firm tongue and beaded papules along the margins of eyelids,who was referred to the deparment of ophthalmology of Kerman university No3: hospital for ophthalmological consultation.pathological examinations of the biopsy specimens from eyelid lesions,confirmed the case as an URBACH-WIETHE disease.
منابع مشابه
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عنوان ژورنال
دوره 3 شماره 3
صفحات 156- 159
تاریخ انتشار 1996-07-01
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